Pediatric Urology Case Reports

99-103

Authors: Umesh Bahadur Singh, Shrikesh Singh, Tanvir Roshan Khan

A wide spectrum of renal, ureteral, and urethral abnormalities has been reported in a patient born with Prune belly syndrome (PBS). The obstruction in the urinary tract can be found anywhere from uppermost (pelviureteral junction) to lowermost (prostatic membranous urethra) urinary tract. The mesenchymal developmental arrest is the main embryological factor responsible for the major features of the syndrome like urethral abnormalities or gastrointestinal abnormalities. PBS patients with urethral obstruction commonly had a patent urachus, because of which such patients survived, early death usually occurred in those patients who did not had a patent urachus. We are reporting an interesting case of prune belly syndrome with superior vesical fissure (an exstrophy variant). To the best of our knowledge this was first reported case of association of two congenital anomalies having common embryological defect process. Presence of superior vesical fissure gives a new insight about the benefits gained by the child for surviving with such fatal congenital anomalies.

108-111

Authors: Metin Gorgu, Ali Gokkaya, Ali Dogan, Jehat Kizilkan, Ertugrul Karanfil

Here, we present a case of hypospadias and median raphe deviation with literature review. A 4-yearold patient presented with subcoronal hypospadias and treated by using tubularized incised plate urethroplasty technique. Additionally, a longitudinal dorsal dartos flap was harvested and transposed to the ventral side by the buttonhole maneuver. The ventral view of the patient penis showed a 15 degree deviation to the right side of the center.

118-121

Authors: Stefania Lasorella, Alberto Verrotti, Luca Zagaroli, Maria Laura Iezzi

Henoch–Schönlein purpura (HSP), also known as immunoglobulin A (IgA) vasculitis, is a systemic vasculitis of unknown cause, mostly affecting children, in which complexes of IgA and components of complement are deposited on arterioles, capillaries, and venules. It is characterized by nonthrombocytopenic palpable purpura, abdominal pain, and arthritis. While renal involvement is well-known and frequent, scrotal involvement is uncommon and, therefore, not easy to be interpreted. Here, we report a case of a 3-year-old boy hospitalized for HSP, presenting with bilateral acute scrotum, and discuss diagnosis and treatment.