Pediatric Urology Case Reports

95-99

Authors: Ruankha Bilommi

Malignant peripheral nerve sheath tumors (MPNST) are rare, aggressive soft tissue sarcomas arising from peripheral nerves that present great challenges to known treatment modalities. Here, we present a case of MPNST involving the dorsum of a penis in a 13-month-old boy. The mass was incomplete excised and a circumcision was performed. Histological study revealed spindle cell tumor of the lesion. Immunohistochemistry showed a strong positive staining for tumor cells. A high grade malignant peripheral nerve sheath tumor was diagnosed.

106-110

Authors: Agnese Roberti, Francesco Turrà, Maria Esposito, Anna Maria Cotrufo, Federica Marinoni, Giovanni Di Iorio

In 1986, Fowler and colleagues described a condition currently known as Fowler's syndrome in young women with unexplained urinary retention associated with polycystic ovary syndrome. Herein, we present a case of a 13-year-old woman diagnosed with Fowler's Syndrome as a result of clinical, radiological and urodynamic electromyogram (EMG) findings. Fowler's syndrome should be considered in the differential diagnosis in children with unexplained chronic urinary retention.

114-118

Authors: Yasar Issi, Sedat Simsik, Unal Bicakci

A four-year-old boy presenting with neuropathic bladder and hydrocephalus developed Fournier’s gangrene of the scrotum and perineum. At first, he was in septic shock and intubated. After debridement and grafting, he was taken to the normal service room from the intensive care unit. He was discharged on the 29th postoperative day. We performed bilateral orchiectomy due to testicular involvement and also repair and flap application to urethra due to its involvement. We think that our case is interesting because Fournier’s gangrene is already rare in children and our case also contains atypical involvement sites such as testes and urethra.