1-6
Congenital giant megaureter associated with ipsilateral multicystic dysplastic kidney in newborn
Authors: Rajendran Ramaswamy, Govinda Ravi, Rayan Baz A, Ghazi Mukattash I, Saif Saeed
Number of views: 562
Congenital giant megaureter presents as abdominal mass and impose diagnostic difficulties. It
can be associated with other upper urinary tract anomalies. A female newborn with antenatal
diagnosis of polycystic kidneys was admitted at birth due to lower abdominal mass. Ultrasound
and CT scans diagnosed a multiloculated cystic lesion in the mid and lower abdomen along with
right side multicystic kidney. At laparotomy, an extaperitoneal, lobulated cystic swelling was
found due to rightside giant megaureter. Its lower end was of normal caliber and orthotopic. End
cutaneous ureterostomy was done. Intravenous urogram and isotope renograms showed
nonfunctioning right kidney. She also had grade II vesicoureteral reflux on left side. Child
suffered urinary infection twice. At 9m age, right nephroureterectomy was done. Histopathologic
examination was consistent with cystic renal dysplasia and dilated ureter. This is the first case
report of giant megaureter associated with ipsilateral multicystic dysplastic kidney in newborn.